PDF | Familial gigantiform cementoma is an exceedingly rare but distinct subtype of cemento-osseous-fibrous lesion. Undocumented. Very few cases of gigantiform cementoma have been reported, and those associated with a positive family history are especially rare. Confusion exists about the. Familial gigantiform cementoma is a rare benign fibrocemento-osseous lesion of the jaws that can cause severe facial deformity. It has an.
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Surgery with recontouring and shaving intent was initially attempted in a local institution about 7 months ago, but in vain. References Publications referenced by this paper. Classification and presentation of a large pedigree. Besides, his pelvis was also considered to be susceptible to fractures because both cortical and trabecular bones were cementomaa a progeric or osteopenic conversion signifying an unexpected calcium loss. NarayanWilfried Wagner Oral surgery, oral medicine, oral pathology and….
Abstract Familial gigantiform cementoma is an exceedingly rare but distinct subtype of cemento-osseous-fibrous lesion.
Familial gigantiform cementoma: classification and presentation of a large pedigree.
Apart from typical multiquadrant and expansile abnormalies involving both jaws, he also suffered from several times of fractures in lower extremity. Since then, supplementation of calcium and vitamin D had been prescribed as a method to ameliorate the general calcium metabolism disorder. Arteriovenous malformation of the scalp with cerebral steal. We present an adolescent case with recurrent familial gigantiform cementoma who received surgical intervention in our hospital.
A The adolescent patient’s aunt who had received surgery nonvascularized iliac bone reconstruction 30 years ago now complaint of anterior maxillary mass with chronic infection. Familial occurrence of periapical cemental dysplasia. Fibro-osseous lesions of the face and jaws. She was yet no exception given her own narratives of femur fracture during adolescence.
Citations Publications citing this paper. Gabali Journal of oral and maxillofacial surgery….
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Surgical removal of the affected bone is needed, and has to be followed by reconstruction. However, owing to such diversion of calcium supply, bone fragility was manifested in the other anatomic regions, especially in lower extremities. Lam Dento maxillo facial radiology From This Paper Figures, tables, and topics from this paper.
Despite the paucity of information regarding FGC, DEA, as we believe, carries diagnostic and therapeutic implications, along with other radiographic examinations.
The radiographic evaluations of lower limb revealed decreased bone density and thinner- or void-cortex structures around fracture regions. ArmstrongPeter Dirks Journal of neurosurgery.
All these results came out with no marked aberrance. You can help Wikipedia by expanding it. The authors report no conflicts of interest.
Citations Publications citing this paper. According to the World Health Organization classification of osseous dysplasias ODFGC is generally regarded as an odontogenic lesion that shares a same periodontal ligament origin with focal, periapical. B Preoperative panorex X-ray showed a characteristic radiographic feature of familial gigantiform cementoma FGC with well-circumscribed radiopaque areas involving all quadrants of the jaw, with mandible being more severely damaged.
Multiquadrant expansile fibro-osseous lesion in a juvenile.
Open in a separate window. Nevertheless, in terms of his description, the progression of disease and related underlying causes has not been clarified.
Dentistry stubs Rare cancers. Fibro-osseous lesions of the head and neck.
OMIM Entry – % – GIGANTIFORM CEMENTOMA, FAMILIAL
Higantiform Search for additional papers on this topic. C Lateral view of FGC. Unfortunately, it is not free to produce. According to the latest World Health Organization WHO classification of cemento-osseous dysplasias CODsFGC is generally characterized by rapid osseous expansion involving all 4 jaw quadrants with predilection for young patients.
All these fractures, which occurred in diaphyseal locations, were categorized to a minor-trauma or spontaneous causes owing to poor evidence of outside forces. In the affected family members, all 4 quadrants were involved.
Suspicious of similar osseous problems in other anatomic locations, we then recommended a pelvic computer tomography CT scan to the patient. A The adolescent patient with a huge mass extending along the mandible body. World Health Organization Classification of Tumours: During the rapid growth phase of FGC in mandible and maxilla, the other bones, especially long bones in lower extremities, were simultaneously undergoing a calcium absorption or transportation problem, as was reflected in the osteoporotic radiographic changes in our adolescent patient.
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